Anti-ACADS antibody (AA39230)

$187.00


Alternative names Short-chain specific acyl-CoA dehydrogenase, mitochondrial, SCAD, EC 1.3.8.1, Butyryl-CoA dehydrogenase, ACADS, ACADS_HUMAN, P16219, 35
Source 412
Species Reactivity Human
Applications IF/ICC, IHC, WB
Host Rabbit
Class Polyclonal
Conjugated Unconjugated


Description

Product name Anti-ACADS antibody (AA39230)
Catalog number AA39230
Brand family Ango
Product type Primary Antibody
Antibody Alternative Names Short-chain specific acyl-CoA dehydrogenase, mitochondrial antibody, SCAD antibody, EC 1.3.8.1 antibody, Butyryl-CoA dehydrogenase antibody, ACADS antibody, ACADS_HUMAN antibody


Biological Information

Immunogen Recombinant protein of human ACADS
Concentration 1 mg/ml
Isotype IgG
Application Notes WB 1:500 - 1:2000 IHC 1:50 - 1:200 IF 1:50 - 1:200
Purification method Purified by affinity chromatography


Target

Target Name ACADS
SwissProt ID Link P16219
Subcellular Location Mitochondrion matrix.
Involvement in Disease Acyl-CoA dehydrogenase short-chain deficiency: An inborn error of mitochondrial fatty acid beta-oxidation resulting in acute acidosis and muscle weakness in infants, and a form of lipid-storage myopathy in adults. The disease is caused by mutations affecting the gene represented in this entry.
Subunit Structure Homotetramer.
Sequence Similarities Belongs to the acyl-CoA dehydrogenase family.


Poduct Presentation

Form Liquid
Preservative 0.02% (w/v) sodium azide
Storage buffer PBS with 50% glycerol, pH 7.3


Storage and Shipping Information

Storage Store at -20 or -80 C. Avoid multiple freeze/thaw cycles.